摘要:
胰腺囊性肿瘤是一类起源于胰腺的囊性病变,约占胰腺肿瘤的2.2%~15.9%[1].广义的囊性肿瘤主要包括:浆液性囊腺瘤(serous cystic neoplasms,SCN),黏液性囊腺瘤(mucinous cystic neoplasms,MCN),实性假乳头状瘤(solid pseudopapillary neoplasms,SPN),导管内乳头状瘤(intra-ductal papillary mucinous neoplasms,IPMN)等.此外,随着CT及MRI等影像学技术的发展,尤其是内镜超声(endo-scopic ultrasound,EUS)下细针穿刺活检技术(fine needle aspiration biopsy,FNAB)的成熟,胰腺囊性肿瘤的检出率与确诊率不断提高,一些特殊类型的胰腺囊性肿瘤,如神经内分泌肿瘤(neuroendocrine neoplasms of the pancreas,NEN),囊性腺泡细胞瘤(cystic acinar cell neoplasms),胰腺淋巴管瘤(lymphangioma of pancreas,LP),导管内管状瘤(intraductal tubular neoplasms,ITN),胰腺血管瘤(angioma-tous neoplasms of the pancreas)等,其生物学特性也逐渐被医生所熟知,并被纳入胰腺囊性肿瘤的范畴[2].