Delayed endolymphatic hydrops (DEH) is a disease entity first described by Kamei and named by Schuknecht,defined as profound sensorineural deafness at early stage and after several years started to appear clinical feature of endolymphatic hydrops such as vertigo,aural fullness like Meniere's disease or fluctuating hearing loss in the contralateral ear.DEH can be classified into ipsilateral type,contralateral type and bilateral type.Although DEH has low incident rate,there are many kinds of etiology and audiology and vestibular tests.Up to now,a lot of literatures about etiology,diagnose,clinical manifestation,relevant examination and therapy of DEH were published abroad.In this review,we will make a summary of research status of DEH.