Corrected Transposition of the Great Arteries with Ebstein’s Anomaly, Dysplasia of the Mitral Leaflets and Persistence of Left Superior Vena Cava in an Adult

• 作者: Angel D. Cueva Aureo Campos-Tello Giancarlo A. Valle Luis M. Milla Nilda Espinola-Zavaleta Oscar García-Rosadio Pablo A. Mendoza Sara Ramirez-Flores
• 来源期刊: 心血管病(英文)
• 学科: 医学
• 关键词: Corrected TRANSPOSITION ECHOCARDIOGRAPHY Ebstein’s ANOMALY Computed Tomography
• 年，卷（期）: 2020,（2）
• 页码范围: 50-56
• 页数: 7页
• 分类号: R54

摘要

Introduction: Congenitally corrected transposition of the great arteries (cc-TGA) is a congenital heart disease rarely described among adult population, especially if it is associated with other abnormalities such as Ebstein’s anomaly and abnormal origin of coronary arteries. Case presentation: Twenty-two-year-old woman admitted to intensive care unit with acute decompensated heart failure. The transthoracic echocardiography demonstrated atrioventricular and ventriculoarterial discordance. The left-sided atrioventricular valve, in this case, the tricuspid valve, showed apical displacement of the septal valve suggesting Ebstein’s anomaly. The computed tomography corroborated these findings and additionally showed a left superior vena cava and an abnormal origin of the coronary arteries. The patient is in NYHA functional class II, receiving treatment with diuretic, digitalis, beta-blockers and angiotensin-converting enzyme (ACE) inhibitor. Conclusion: This is a very interesting case of an adult in the third decade of life with cc-TGA associated with abnormalities not described in the literature that had reached adulthood. Noninvasive images play an important role in its diagnosis.