Chronic thromboembolic pulmonary hypertension related to hemangiolymphangioma

• 作者: Chika Kitaoka Chisato Akita Giyo Ko Keita Tamanuki Masato Oguri Toshimi Nakamura Tsuneyuki Nakamura Yutaka Saikawa
• 来源期刊: 临床医学病理报告(英文)
• 学科: 医学
• 关键词: Hemangiolymphangioma CHRONIC THROMBOEMBOLIC PULMONARY HYPERTENSION LONG-TERM FOLLOW-UP
• 年，卷（期）: 2014,（1）
• 页码范围: 36-37
• 页数: 2页
• 分类号: R5

摘要

Hemangiolymphangioma (HL) is a congenital anomaly and histologically benign tumor, which was composed of both the lymphatic and the blood vessels. We report an adult case of HL complicated by chronic thromboembolic pulmonary hypertension (CTEPH) in a 20-year-old female. Gastrointestinal bleeding scintigraphy and operative findings elucidate a close relationship between CTEPH and residual HL. This case indicates that HL survivors with remaining left-to-right shunt might lead to CTEPH during the long-term follow-up.