<strong><span style="font-family:Verdana;">Introduction: </span></strong><span style="font-family:;" "=""><span style="font-family:Verdana;">Pulmonary agenesis is a rare congenital abnormality defined by the absence of parenchyma, bronchi and pulmonary vessels, frequently associated with other malformations. We describe a case of isolated right pulmonary agenesis diagnosed in the pediatric ward of the Mali Hospital. </span><b><span style="font-family:Verdana;">Clinical case</span></b><span style="font-family:Verdana;">: He was a month-old baby boy, born at term by cesarean section of a well-followed pregnancy. He was not resuscitated. He developed dyspnea after a cold. An emergency chest X-ray revealed a right opaque lung. He was referred to the hospital for the exploration of this opacity. At the entrance, it weighed 3910 g, size: 54 cm and the temperature was 36.9<span style="white-space:nowrap;">°</span>C. He had a polypnea, an intercostal print. The sounds of the heart were diverted to the right. The rest of the clinical examination was without much particularity. The chest CT scan confirmed the right pulmonary agenesis. Abdominal and cardiac ultrasound w</span></span><span style="font-family:Verdana;">as</span><span style="font-family:Verdana;"> normal. </span><span style="font-family:Verdana;">A healing includ</span><span style="font-family:Verdana;">es</span><span style="font-family:Verdana;"> oxygenotherapy, serum glucose 10% minding 100 ml/ Kg/day and amoxicillin</span><span style="font-family:;" "=""> </span><span style="font-family:Verdana;">minding 100 mg/ Kg/day</span><span style="font-family:;" "=""> </span><span style="font-family:Verdana;">at 3 times by oral way</span><span style="font-family:Verdana;">. After 24 hours of treatment</span><span style="font-family:Verdana;">,</span><span style="font-family:Verdana;"> we observed an improvement in dyspnea. On D2</span><span style="font-family:Verdana;">,</span><span style="font-family:;" "=""><span style="font-family:Verdana;"> he was weaned off oxy