Signet Ring Cell Carcinoma of Ampulla of Vater: Report of a Rare Malignancy and Literature Review

• 作者: Afaf Amarti Hassania Ameurtesse Hinde El Fatemi Ihsane Souaf Imane Hafid Kawtar Znati Leila Chbani Nawale Hammas Sanae Chahbouni Tawfik Harmouch
• 来源期刊: 临床医学病理报告(英文)
• 学科: 医学
• 关键词: AMPULLA of VATER Carcinoma Signet Ring Cell PANCREAS
• 年，卷（期）: lcyxblbgyw_2014,（3）
• 页码范围: 145-148
• 页数: 4页
• 分类号: R73

摘要

Introduction: Signet ring cell carcinoma is a rare tumor that generally originates in the gastrointestinal tract. Signet-ring cell carcinoma of the ampulla of Vater is extremely uncommon and a very rare clinical entity, which is infrequently reported in medical literature and only 31 cases have been mentioned. Most tumors affecting Vater’s Ampulla are adenocarcinomas and other histological variants are less frequent. It mainly occurs in elderly patients. Case Presentation: We report a case of signet ring cell carcinoma of Vater’s Ampulla. The tumour had infiltrated the duodenal, but local lymph nodes were clear (T3N0M0). Duodenopancreatectomy with pylorus preservation is the treatment of choice. Conclusions: Etiology and survival are not well-defined in the literature due to the extreme rarity of this disease.