Lipomatous Medulloblastoma: A Case Report

• 作者: Alpha Boubacar Bah Hammas Nawal Ibrahima Berete Khalid Chakour Mohammed Benzagmout Mohammed Faiz Chaoui Seylan Diawara
• 来源期刊: 现代神经外科学进展(英文)
• 学科: 医学
• 关键词: MEDULLOBLASTOMA Lipomatous Liponeurocytoma POSTERIOR Fossa TUMOR Suboccipital CRANIOTOMY
• 年，卷（期）: xdsjwkxjzyw_2019,（4）
• 页码范围: 452-456
• 页数: 5页
• 分类号: R73

摘要

Lipomatous medulloblastoma is not a separate entity but apparently distinct variant of medulloblastoma. Since the first case report in 1978 by Bechtel et al. [1], few cases have been published. We report an additional case of a 52-year-old right-handed man presented to the emergency department with evaluation of progressive severe intracranial hypertension and ataxia. His past medical history was unremarkable. His physical examination showed cerebellar syndromes. He underwent magnetic resonance imaging (MRI) which revealed a unique mass in the posterior fossa, lying within a cerebellar hemisphere. The patient underwent a suboccipital craniotomy for with a complete resection and samples were sent for histologic examination, showing closely packed, and round to oval cells. The nuclei had an irregular shape with clumps of heterochromatin. Lipid accumulation was a prominent feature of neoplastic cells. Postoperatively the patient did not receive fractionated radiotherapy. He is alive without deficit and with no evidence of recurrence on neuroimaging.