Bernard-Soulier Syndrome in Pregnancy: A Case Report

• 作者: Amanda Vilaverde Perez Cilomar Martins de Oliveira Filho Daniela Vanessa Vettori Edimárlei Gonsales Valério Fernanda Grossi Janete Vettorazzi Mariana Sbaraini Sheila Nogueira do Amaral Tássia Cividanes Pazinato
• 来源期刊: 妇产科期刊(英文)
• 学科: 医学
• 关键词: Bernard-Soulier HEMOSTASIS THROMBOCYTOPENIA PREGNANCY OBSTETRICS POSTPARTUM HEMORRHAGE
• 年，卷（期）: 2019,（6）
• 页码范围: 838-844
• 页数: 7页
• 分类号: R73

摘要

Background: Bernard-Soulier Syndrome (BSS) is a rare autosomal recessively inherited bleeding disorder of platelet function. Pregnancy in BSS is associated with a high risk of serious bleeding for both mother and neonate, and current data show no consensual approach. Aim: To report the case of a pregnant woman with BSS, in order to provide more information about management of these cases. Case Presentation: This case report describes a successful pregnancy outcome in a woman with BSS who was closely monitored throughout pregnancy and postpartum period, and had a judiciously planned birth. Conclusion: Management of BSS during pregnancy is still unclear. However, it is important to strictly control platelet counts and plan the birth in advance.