Uethral duplication is very rare congenital anomaly with ill defined etiology. Very few cases have been reported in literature till date. Patients may present with urinary incontinence, abnormal or dual urinary stream, recurrent urinary tract infections and sometimes associated penile deformity. Aim of presenting this case report is to limelight one of such rare presentations. Herewith reporting a case of 16 months old baby boy presented with history of recurrent urinary tract infection, solitary kidney with grade 4 primary vesico-ureteric reflux and duplication of urethra. Diagnosis and treatment plan in such cases require a multistage approach.