Thymic langerhans cell histiocytosis in children: A case report

• 作者: Camille Chabert Jean Pierre Pracros Marie Poncelet Perrine Marec Berard
• 来源期刊: 儿科学期刊(英文)
• 学科: 医学
• 关键词: LANGERHANS Cell HISTIOCYTOSIS CHILDREN THYMUS
• 年，卷（期）: 2012,（4）
• 页码范围: 303-305
• 页数: 3页
• 分类号: R73

摘要

Langerhans cell histiocytosis has long been described as a rare systemic disorder involving the proliferation of Langerhans cells with formation of granuloma. The disease may be localised or diffuse. Typical forms of the disease involving the bone, the skin or the pituitary gland have been well described whereas others, such as thymic histiocytosis, are still poorly understood. Here, we report a case of isolated Langerhans cell histiocytosis of the thymus in an infant with non-specific symptoms. We provide a description of the disease and discuss patient management.