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摘要:
Background: There is an increasing recognition of patients with Ehlers Danlos Syndromes. The laxity of the ligaments and the weakness of the connective tissue has resulted in increasing number of patients requiring surgical intervention. Ehlers Danlos Syndromes are not about hypermobile joints only, they are associated with multiple co-existing conditions such as Chiari malformation, Tethered Cord Syndrome, spinal instability, abdominal pain, Dysautonomia and Mast Cell Activation Syndrome. The combined incidence of Ehlers Danlos Syndromes is 1 in 5000 people. Most experts believe that the actual incidence is much higher. Many of these cases are under-diagnosed. Nevertheless, patients with Ehlers Danlos Syndromes, diagnosed or undiagnosed often require surgical intervention. This review article has been written to shed light on the need for special consideration during anesthesia. Objectives: Our objective was to conduct a review of anesthetic considerations in patients with Ehlers Danlos Syndromes. Study Design: We used a narrative review design. Methods: This review was done using searches of PubMed, MEDLINE/OVID, SCOPUS, and manual searches of the bibliographies of known primary and review articles from inception to 2019. Other data sources included hand searches of publications driven by manuscript authors. Search terms included concepts of “Ehlers Danlos Syndrome”, “EDS”, “pain”, “anesthesia”, “surgery” and combination of terms. Search method was not restricted to any one language. Results: Articles were screened by title, abstract, and full article review. They were then analyzed by specific clinical indications and appropriate data was presented based on critical analysis of those articles. Limitations: More studies about the effect of anesthetic techniques and Ehlers Danlos Syndromes are required. Conclusions: Patients with Ehlers Danlos Syndromes may present with an array of coexisting medical conditions such as Dysautonomia, Mast Cell Activation Syndrome, Chiari Malformation, Tethered
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篇名 Perioperative Care in Patients with Ehlers Danlos Syndromes
来源期刊 麻醉学期刊(英文) 学科 医学
关键词 Anesthesia Ehlers Danlos SYNDROMES POTS MCAS Mast Cell Activation SYNDROME POSTURAL ORTHOSTATIC TACHYCARDIA SYNDROME
年,卷(期) 2020,(1) 所属期刊栏目
研究方向 页码范围 13-29
页数 17页 分类号 R73
字数 语种
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Anesthesia
Ehlers
Danlos
SYNDROMES
POTS
MCAS
Mast
Cell
Activation
SYNDROME
POSTURAL
ORTHOSTATIC
TACHYCARDIA
SYNDROME
研究起点
研究来源
研究分支
研究去脉
引文网络交叉学科
相关学者/机构
期刊影响力
麻醉学期刊(英文)
月刊
2164-5531
武汉市江夏区汤逊湖北路38号光谷总部空间
出版文献量(篇)
92
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0
总被引数(次)
0
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